Lymphangioleiomyomatosis in a Young Male
Published: January 1, 2020 | DOI: https://doi.org/10.7860/JCDR/2020/43159.13424
Vishwanath Pujari, Sanchit Mohan, Priti Meshram, Rohit Hegde
1. Associate Professor, Department of Pulmonary Medicine, Grant Government Medical College, Mumbai, Maharashtra, India.
2. Junior Resident, Department of Pulmonary Medicine, Grant Government Medical College, Mumbai, Maharashtra, India.
3. Head, Department of Pulmonary Medicine, Grant Government Medical College, Mumbai, Maharashtra, India.
4. Associate Professor, Department of Pulmonary Medicine, Grant Government Medical College, Mumbai, Maharashtra, India.
Correspondence
Dr. Sanchit Mohan,
110,300, Resident Hostel, JJ Hospital, Byculla, Mumbai, Maharashtra, India.
E-mail: sanchit.agarwal1992@gmail.com
Lymphangioleiomyomatosis (LAM) is a rare multisystem disorder, predominantly affecting females in the reproductive age group, characterised by multiple cysts in lungs. A 15-year-old male was admitted in our institute for right sided renal mass for which he underwent right nephrectomy and was referred to our department for bilateral spontaneous pneumothoraces. CT thorax was done which showed bilateral pneumothoraces with multiple thin walled cysts and subtle ground glass opacities in both lung fields suggestive of changes of LAM. LAM is rarely seen in males, however if present ER/PR status can help in modifying the management. This is the youngest case of LAM reported in a male worldwide.
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